X123 Antibody (3C7): sc-100741

X123 Antibody (3C7) is a mouse monoclonal IgG2a kappa light chain antibody that detects X123 protein of mouse, rat, and human origin by western blotting (WB), immunoprecipitation (IP), and enzyme-linked immunosorbent assay (ELISA). X123 (3C7) antibody is available as the non-conjugated form. X123, also known as C9orf61 (chromosome 9 open reading frame 61), plays a crucial role in cellular processes, particularly in Friedreich′s ataxia, a hereditary condition characterized by the degeneration of spinal cord and nerve tissue. This 289 amino acid protein is predominantly expressed in skeletal muscle, with lower expression levels found in the brain, heart, and lung, indicating significant involvement in muscle function and health. The gene encoding X123 is situated within the Friedreich′s ataxia region on chromosome 9, suggesting that alterations in X123 may contribute to the disease′s pathogenesis. Understanding X123 function and expression may provide insights into potential therapeutic targets for managing Friedreich′s ataxia and related disorders.

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X123 Antibody (3C7) References:

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