Phenyl α-L-iduronide cyclohexylammonium salt (CAS 39031-70-4)
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Phenyl α-L-iduronide cyclohexylammonium salt is a compound that functions as an inhibitor in biochemical. It acts by competitively inhibiting the activity of certain enzymes involved in glycosaminoglycan metabolism. This inhibition disrupts the normal breakdown of glycosaminoglycans, leading to the accumulation of these molecules within cells. This accumulation can be used to study the effects of glycosaminoglycan storage disorders. At the molecular level, the compound binds to the active site of the enzyme, preventing the substrate from binding and inhibiting the catalytic activity. This mechanism of action allows to study the specific role of these enzymes in cellular processes. Phenyl α-L-iduronide cyclohexylammonium salt plays a functional role in inhibiting enzyme activity and studying glycosaminoglycan metabolism in experimental applications.
Phenyl α-L-iduronide cyclohexylammonium salt (CAS 39031-70-4) References
- Prenatal diagnosis of the Hurler syndrome: report on 40 pregnancies at risk. | Kleijer, WJ., et al. 1983. Prenat Diagn. 3: 179-86. PMID: 6413967
- Comparison of the substrate 4-methylumbelliferyl-alpha-l-iduronide with phenyl-alpha-L-iduronide for the diagnosis of Hurler's disease in cultured cells. | Butterworth, J. and Broadhead, DM. 1980. J Inherit Metab Dis. 2: 71-4. PMID: 6796763
- The Hurler syndrome: detection of patients and heterozygotes using a microassay for alpha-L-iduronidase in fibroblasts. | Kleijer, WJ., et al. 1981. Clin Chim Acta. 116: 47-54. PMID: 6797759
Ordering Information
| Product Name | Catalog # | UNIT | Price | Qty | FAVORITES | |
Phenyl α-L-iduronide cyclohexylammonium salt, 5 mg | sc-215705 | 5 mg | $235.00 |