ACCÈS RAPIDE AUX LIENS
VOIR ÉGALEMENT...
IVD (Isovaleryl-CoA dehydrogenase, mitochondrial) is a 423 amino acid protein encoded by the human gene IVD. IVD is a mitochondrion matrix protein that belongs to the acyl-CoA dehydrogenase family. IVD is a homotetrameric flavoenzyme which catalyzes the conversion of isovaleryl-CoA to 3-methylcrotonyl-CoA. Defects of the IVD gene lead to ineffective isoforms that are the underlying cause of isovaleric acidemia. Two forms of isovaleric acidemia, possibly allelic, are recognized: the acute neonatal form, leading to massive metabolic acidosis from the first days of life and rapid death, and a chronic form in which periodic attacks of severe ketoacidosis occur with asymptomatic intervening periods. There are seven classes of mutants, each with different deletions and pathologies.
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Informations pour la commande
Nom du produit | Ref. Catalogue | COND. | Prix HT | QTÉ | Favoris | |
Anticorps IVD (B-9) | sc-271205 | 200 µg/ml | $316.00 | |||
IVD (B-9): m-IgG Fc BP-HRP Kit | sc-537589 | 200 µg Ab; 10 µg BP | $354.00 | |||
IVD (B-9): m-IgGκ BP-HRP Kit | sc-534896 | 200 µg Ab; 40 µg BP | $354.00 | |||
IVD (B-9): m-IgG1 BP-HRP Kit | sc-545247 | 200 µg Ab; 20 µg BP | $354.00 | |||
IVD (B-9) peptide neutralisant | sc-271205 P | 100 µg/0.5 ml | $68.00 |