Aktivator von:
1190007I07Rik, AARS2, ADCK4, AFG3L2, ANT1, ATP5G3, C20orf7, C20orf72, CABC1, CHCHD4, CLS1, COA6, COQ10B, DNA pol γ2, ETHE1, FASTKD3, FASTKD5, GTPBP3, HtrA2, LETM2, LONP1, Mcsp, Mel13, Metaxin 1, mitochondrial ferritin, Mitofilin, MPV17L2, MRP-L10, MRP-L12, MRP-L13, MRP-L18, MRP-L24, MRP-L3, MRP-L40, MRP-L44, MRP-S25, MRP-S26, MRRF, ND6, NDUFA6, NDUFA8, NDUFAF3, NDUFAF7, NDUFS7, NDUFS8, Oma1, OXA1L, p22-phox, p60 Mitochondrial Marker, PARS2, PITRM1, PRX III, PYROXD2, SFXN5, Sptrx-1, SPTRX-3, SSBP1, TAMM41, TFB2M, Tim22, Tim8A, Tim8B, TMEM126A, TMEM135, Tom20, Tom22, Tom40B, Tomm5, TTC19, TTC34, UQCRHL, und XRCC6BP1.