Aktivator von:
α-KGD, β-Galactose Dehydrogenase, γ-sarcoglycan, μ-crystallin, 1190007I07Rik, 1810026J23Rik, 1810043H04Rik, 20S Proteasome α2, 20S Proteasome β5, 2900010M23Rik, 3-Hydroxybutyrate Dehydrogenase, A230051G13Rik, AARS2, Aasdh, ABCB8, ACAA2, ACAD-12, ACAD-9, ACADSB, ACMSD, ACO2, ACRV1, ACSF3, ACSM2A, ACSVL2, AGXT2L2, AI-BP, AIFL, AK1, AK7, AK8, ALDH5A1, ALS2CR11, AMID, AMPD1, AMPD3, ANT1, apoO, ARMD8, ATAD4, ATP11, ATP5 (Complex V; Mitochondrial ATP synthase), ATP5D, ATP5G3, ATP8, ATPAF2, BBS1, BCS1L, BDH1, BFZB, BRP44L, C030010C08Rik, C11orf83, C20orf111, C20orf165, C20orf3, C20orf7, C3orf60, C4orf14, C6orf167, C8orf38, CABC1, CBR4, CEACAM16, CHCHD10, CHCHD3, CHCHD4, CHCHD6, CHCHD8, citrin, CKMT1, CKMT1A, CLYBL, CMC1, COA1, COA5, COA6, COQ10B, COQ2, COQ4, COQ5, COQ6, COQ7, COQ9, COX11, COX15, COX18, COX4I2, COX5a, COX6a2, COX7a2L, COX7b, COX7b2, COX8b, COX8c, creatine kinase-B, CRIF1, CROT, CRP2BP, CtBP1, CTL2, CYB561D2, CYB5R2, CYB5R3, Cyclophilin F, Cystinosin, cytochrome b5 type B, cytochrome b561, Cytochrome C, D10Jhu81e, D2HGDH, DCAF15, DECR1, DFNB59, DGUOK, DHDH, DHRS1, DHRS12, DHRS7, DHRSX, DHS, dinitrophenol, DIO1, DNA pol γ2, DNC, DSC2, DTWD1, ECH1, EFTA, EG436008, EG546368, EG667693, ENOSF1, ERAL1, Eso-1, ETHE1, FAM213A, FANCE, FAP, FASTKD1, FASTKD3, FASTKD5, Fdx1, FDX1L, FOXRED1, FOXRED2, Fumarylacetoacetase, GABP-β2, GCH-I, GDAP1, GDAP1L1, GHITM, GlyRS, GPD2, Grim19, group IVF sPLA2, GTPBP3, GUF1, HACL1, HADHB, HADHSC, Headpin, HIBCH, Hint2, HSDL1, HSPE1-MOB4, HtrA2, IDH3A, IgE, IMMP1L, ISCA1, KHNYN, KIAA1462, L2HGDH, LACE1, LEPREL4, LIAS, Lipoic Acid, LIPT1, LIPT2, LOC100041273, LONP1, LPAAT-δ, LRP130, LYCAT, LYRM4, MCART1, MCART2, MCCA, Mcsp, MDH1B, ME3, Metaxin 1, Metaxin 2, Mfn2, MGC52110, MGP, mHMGCS, Mimitin, Miner2, Misato, Mitochondrial CysRs, mitochondrial ferritin, Mitochondrial Inner Membrane, Mitofilin, MOCS3, MPV17, MPV17L, MRM1, MRP-L10, MRP-L12, MRP-L13, MRP-L15, MRP-L18, MRP-L19, MRP-L2, MRP-L24, MRP-L27, MRP-L28, MRP-L3, MRP-L35, MRP-L40, MRP-L42, MRP-L43, MRP-L48, MRP-L49, MRP-L53, MRP-L54, MRP-L9, MRP-S10, MRP-S12, MRP-S15, MRP-S22, MRP-S23, MRP-S25, MRP-S26, MRP-S27, MRP-S30, MRP-S35, MRP-S36, MRP-S5, MRP-S9, MRRF, mt-Atp8, MTO1, MTP18, MTRNR2L10, MTRNR2L2, MTRNR2L3, MTRNR2L4, MTRNR2L6, MTRNR2L7, MtRPOL, Muskelin, MVD, Myo-inositol oxygenase, NARFL, NCB5OR, ND1, ND2, ND3, ND4, ND5, ND6, NDOR1, NDUFA1, NDUFA10, NDUFA11, NDUFA12, NDUFA2, NDUFA4, NDUFA4L2, NDUFA5, NDUFA6, NDUFA7, NDUFA8, NDUFA9, NDUFAB1, NDUFAF3, NDUFAF6, NDUFAF7, NDUFB1, NDUFB10, NDUFB11, NDUFB2, NDUFB4, NDUFB5, NDUFB6, NDUFB7, NDUFB8, NDUFB9, NDUFC1, NDUFS1, NDUFS2, NDUFS3, NDUFS4, NDUFS5, NDUFS6, NDUFS7, NDUFV1, NDUFV3, Nebulin, NHN1, NIP30, nm23-H4, NMNAT-3, NSUN3, NT5C1A, NUDCD3, NUDT18, Nulp1, ODF3B, OR11L1, OSCP, OSCP1, OXA1L, Oxr1, p60 Mitochondrial Marker, PACRG, PAH, PAP-β, Paraplegin, PARS2, PDSS1, Penumbra, PET100, Pet117, PGAM5, PGK2, PGS1, PGs2_5730494M16Rik, PINK1, PISD, PITRM1, PMPCB, PNP2, POLR2J1, PON2, PPAN, PQLC1, PRODH, PROSC, PRX III, PTCD1, PWP2, PYROXD2, QCR10, QIL1, RBM Y chromosome, RBMY1A1, Renalase, retinitis pigmentosa 1, RG9MTD1, RMND1, ROPN1, RPUSD2, RPUSD4, Sam50, Sarcospan, SCAF1, SCARA3, SCO2, SDHA, SDHAF1, SDHAF2, SDHB, SDHC, SDHD, SELENBP1, SFXN2, SFXN4, SLC25A11, SLC25A14, SLC25A18, SLC25A22, SLC25A25, SLC25A38, SLC25A41, SLC25A43, SOD-3, SPACA7, SPANX-N4, SPATA18, SPATA25, SPATA9, Spatacsin, SPERT, SQRDL, SSBP1, STOML1, SUCLG2, SURF-1, SUV3, symplekin, synphilin-1, Tafazzin, TARSL1, TCP-11, TCP11, TERE1, TEX29, TEX30, TEX9, TFB1M, TFB2M, THTR2, Tim13A/B, Tim13B, Tim14, Tim22, Tim23, Tim8A, Tim8B, Timm8a2, TMEM126A, TMEM135, TMEM14B, TMEM60, TMEM8C, TMIE, Tom22, Tom34, Tom40, Tom7, Tomm5, TRAP-1, Treacle, Tropomyosin, TSARG1, TTC19, TTC34, UBE2G2, UBTFL1, UCP4, UCRC, uMtCK, UQCRB, UQCRC1, UQCRC2, UQCRH, UQCRHL, USMG5, USP30, vanin-3, VAT1L, VKOR, VKORC1L1, WARS2, WDR60, XRCC6BP1, YME1L1, und ZADH2.